Keywords
tetralogy of Fallot
adult congenital heart disease
How to Cite
Abstract
We present the case of a 24-year-old male patient with a history of correction of
tetralogy of Fallot when he was 2. He reports presenting 6 syncopal episodes during
the last 6 months. Therefore, a transthoracic color Doppler echocardiogram was
performed, reporting right ventricular dilatation, mild global deterioration of the
right ventricular systolic function, absent pulmonary valve with severe insufficiency,
and free passage. A diagnosis of absent pulmonary valve with severe valvular
insufficiency was made. Surgical treatment was performed by placing an aortic
bioprosthesis (stentless) No. 25, Medtronic FreestyleTM, in the pulmonary position.
The patient evolved favorably and was discharged without complications on the
fourth postoperative day. In addition, a brief bibliographic review of the disease is
made.
References
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Apitz C, Weeb GD, Redington AN. Tetralogía de Fallot. Lancet. 2009;374: 1462-1471.
Karl TR, Musumeci F, de Leval M, et al. Surgical treatment of absent pulmonary valve syndrome. J Thorac Cardiovasc Surg. 1986 Apr.91(4):590-7.
Snir E, de Leval MR, Elliott MJ, Stark J. Current surgical technique to repair Fallot's tetralogy with absent pulmonary valve syndrome. Ann Thorac Surg. 1991 Jun. 51(6):979-82.