Abstract
Heart valve diseases are multifactorial conditions with a significant genetic and/or hereditary component. In such cases, structural alterations of the aortic valve are often observed, including a supernumerary cusp that forms a quadricuspid valve. This anomaly is closely associated with the onset and progression of aortic regurgitation, even under optimal medical management. In a small proportion of patients, the quadricuspid valve may also be associated with aortic stenosis.
A quadricuspid aortic valve is usually discovered incidentally, most often in the sixth decade of life.
We report the case of a female patient with a quadricuspid valve associated with válvula aórtica cuadricúspide, insuficiencia aórtica, malformación
cardíaca congénitasevere type II aortic regurgitation
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